Pyknocytosis
Piknositosis ko ngonka hematoloji, kañum ne ina waɗi piknositosis e nder ƴiiƴam. Piknositteeji ko ƴiye boɗeeje peeñɗe e mbaydi mbaylaandi, ɗe njuumtaani, tokoose ɗe mbaydiiji mum en ngonaa no haanirta nii, ɗe nganndu-ɗaa ko ganndo safaara tan waawi anndude ɗe, kadi annduɗo patoloji hoolkisa ɗum en e ƴeewndo ƴiiƴam periferik.[1]
Piknositosis cukalel ko ñawu ɓurngu heewde jokkondirde, kadi ko ñawu hematoloji sukaaɓe seeɗa. Ko ɗum huunde waawnde saabaade ŋakkere ƴiiƴam e nder sukaaɓe jibinaaɓe. Piknositosis cukalel ina heewi feeñde e ɓuuɓri sukaaɓe e ŋakkere ƴiiƴam tiiɗnde, ina heewi ɗaɓɓude ƴiiƴam. Anemia hemolitik jokkondirɗo e mum ina heewi juutde e ɓuuɓde e nder yontereeji 3-4, tawa ina safra e hoore mum, ina timma e lebbi nay haa jeegom nguurndam. Etiyoloji ooɗoo sifaa tabitinaaka kono won hujjaaji, ina jeyaa heen woodgol ƴiiƴam mboɗejam ɓuuɓɗam e ƴiiƴam periferik nannduɗam e mboros oksidaa, ina hollita sabaabuuji baɗɗi ŋakkeende antioksidaaji ko wayi no witamin E walla woodgol faktor oksidaa. Ñawndugol piknositosis cukalel ina tuugii e ƴiiƴam periferik, tawa ina waɗi wiɗtooji ɓeydotooɗi ngam safrude ngonkaaji nannduɗi e ɗuum, ko wayi no ŋakkeende glukos-6-fosfaat dehidrogenase e ŋakkeende piruwat kinase. Ɗeeɗoo geɗe ɗiɗi fof ina mbaawi kadi addande piknositteeji yiyteteeɗi e ƴiiƴam. [2] oo ina waɗi fototerapi so tawii tolno bilirubin e nder ƴiiƴam ina ɓura duuɓi cukalel ngel, e ƴiiƴam so tawii hemoglobin ina tawaa ina famɗi no jaɓaaka walla ina ustoo tuugnaade e ƴeewndo safaara e nafooje laboratuwaar.[citation needed][3]
Tuugnorgal
[taƴto | taƴto ɗaɗi wiki]- ↑ Eyssette-Guerreau, Stephanie; Bader-Meunier, Brigitte; Garcon, Loic; Guitton, C.; Cynober, Therese (2006). "Infantile pyknocytosis: A cause of haemolytic anaemia of the newborn". British Journal of Haematology. 133 (4): 439–42. doi:10.1111/j.1365-2141.2006.06033.x. PMID 16643454. S2CID 20150031.
- ↑ Limme, B.; Dresse, M.-F.; Ketelslegers, O.; Rigo, V.; Hoyoux, C. (2008). "La pyknocytose infantile : Une anémie néonatale mal connue à propos de 5 cas" [Infantile pyknocytosis: A rare form of neonatal hemolytic anemia. 5 case-studies]. Archives de Pédiatrie (in French). 15 (12): 1765–8. doi:10.1016/j.arcped.2008.09.012. PMID 18995999.CS1 maint: unrecognized language (link)
- ↑ Eyssette-Guerreau, Stephanie; Bader-Meunier, Brigitte; Garcon, Loic; Guitton, C.; Cynober, Therese (2006). "Infantile pyknocytosis: A cause of haemolytic anaemia of the newborn". British Journal of Haematology. 133 (4): 439–42. doi:10.1111/j.1365-2141.2006.06033.x. PMID 16643454. S2CID 20150031.